A 44-Year-Old Man with Fever, Mucocutaneous Ulcers, and a Rash

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Meghan J Ho MD
Ines Sherifi
Rodrigo Cavalcanti MSc MD

Keywords

Behcet’s disease, mucocutaneous ulcers, pharyngitis, cervical lymphadenopathy

Abstract

We report the case of a 44-year-old man who presented with mucocutaneous ulcers, purpuric rash, fever, pharyngitis, cervical lymphadenopathy, and arthralgias. The patient’s symptoms resolved with prednisone treatment. He later experienced recurrence of oral ulcers that responded to colchicine treatment. Behcet’s disease is a systemic vasculitis characterized by recurring oral and genital mucocutaneous lesions and accompanying ocular, gastrointestinal, articular, pulmonary, neurologic, or peripheral vascular manifestations. Sweet’s syndrome typically presents with flulike symptoms, fever, neutrophilia, and painful erythematous skin lesions. Along with skin biopsy, classification criteria exist for both conditions, which may help differentiate the two diagnoses on initial presentation.
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